Sweet-smelling urine may be a sign of uncontrolled diabetes or a rare disease of metabolism. Liver disease and certain metabolic disorders may cause musty-smelling urine. Some conditions that can cause changes in urine odor include: Bladder fistula.
Babies with MSUD are unable to break down amino acids called leucine, isoleucine and valine. Very high levels of these amino acids are harmful. One of the characteristic symptoms of MSUD is sweet-smelling urine, which gives the condition its name.
Outside of diabetes, there are other reasons why your urine (pee) may smell sweet, including bacterial urinary tract infections (UTIs), liver disease, and a rare genetic disorder called maple syrup urine disease.
Liver disease
Infections and diseases of the liver can produce high ammonia levels in the urine and the accompanying pungent odor. Ammonia levels in blood and urine will increase when the liver is not working as it should. Any continued ammonia odor in urine should be checked by a doctor.
Ketones smell like acetone – like pear drops, or like nail-polish remover. DKA usually occurs in people with Type 1 diabetes, and is a medical emergency. "If diabetes remains undiagnosed or poorly controlled, high levels of glucose in the urine may make the urine smell sweet."
Sweet-smelling urine may be a sign of uncontrolled diabetes or a rare disease of metabolism. Liver disease and certain metabolic disorders may cause musty-smelling urine. Some conditions that can cause changes in urine odor include: Bladder fistula.
What Does Diabetic Urine Smell Like? One warning sign of diabetes or high blood sugar is urine that smells sweet or fruity. The sweetness comes from sugar in your urine and is a sign your body is trying to get rid of extra sugar in your blood.
Well, the easy answer is; As your body processes a bowl of sugar puffs, your kidneys have a hard time breaking down the sugars so they pass on through into your wee, which gives it the sweet aroma.
Maple syrup urine disease (MSUD) is a disorder in which the body cannot break down certain parts of proteins. The urine of people with this condition can smell like maple syrup.
If you have diabetes, a change in body odor could be a sign of diabetes-related ketoacidosis. High ketone levels cause your blood to become acidic and your body odor to be fruity. In the case of liver or kidney disease, your odor may give off a bleach-like smell due to toxin buildup in your body.
Smelling of the breath is common after having certain food or in the morning, but with people suffering from fatty liver conditions, it remains throughout the day. The breath may have a distinct sulfur and musty smell throughout the day. It is an obvious sign of fatty liver disease and should not be ignored.
Foetor hepaticus is a feature of severe liver disease; a sweet and musty smell both on the breath and in urine. It is caused by the excretion of dimethyl disulphide and methyl mercaptan (CH3SH)2, arising from an excess of methionine.
Trimethylaminuria (TMAU) is an uncommon condition that causes an unpleasant, fishy smell. It's also called "fish odour syndrome". Sometimes it's caused by faulty genes that a person inherits from their parents, but this isn't always the case. There's currently no cure, but there are things that can help.
When a person eats a lot of protein instead of carbohydrates, their body uses protein and stored fat for energy instead of using carbohydrates as it would usually do. As a result, the ketone level in the blood will rise. When these ketones leave the body in the urine, the urine may smell sweet or similar to popcorn.
The scent of fetor hepaticus is more distinct and smells like sulfur. It happens as a result of liver disease. Learn more about fetor hepaticus and how to manage the condition.
What Are the Symptoms of Maple Syrup Urine Disease? The most distinct and easily recognizable symptom of MSUD is the smell. Urine, sweat, and even the earwax of people with MSUD will often have a sweet smell similar to maple syrup or burnt sugar.
Pee that smells like ammonia
If you detect a hint of ammonia in your urine, it could be a sign of a urinary tract infection (UTI). The odor suggests that bacteria may be swimming around in your urinary system, most likely in your urethra, kidneys or bladder.
Sometimes, unusual urine odor indicates a medical condition or disease, such as: Cystitis (bladder inflammation) Dehydration (which is when the body doesn't have enough water and other fluids to work properly) Diabetic ketoacidosis.
If you have diabetes insipidus, you'll continue to pee large amounts of watery (dilute), light-colored urine when normally you'd only pee a small amount of concentrated, dark yellow urine.
With advanced diabetes, sugar and ketones, which are normally absent, can accumulate in the urine and create a strong odor.